Abstracts

Rationale: Perisilvian polimicrogyria is a cerebral malformation characterized by excessive cortical folds and slightly deep solci. The microscopic examination shows an abnormal stratum structure of the cerebral cortex. The topographic distribution has great variability, but bilateral perisilvian polimicrogyria is the most common one. It might declare as an Opercular Syndrome in adults, and in children is Worster Drought Syndrome, is rare, which consists of a disorder of the voluntary control of facial, tongue, pharinx and masticatory muscles, as well as slight mental retardation, epilepsy and pseudobulbar palsy. Methods: We realize a review of the cases diagnose of Opercular Syndrome (Worster Drought) in Neuropaediatric's Service of the University Hospital Vall D Hebron, during 1995-2006. There were included in this study patients who presented convulsive episodes during the evolution of his(her,your) disease. We make a record of the cerebral activity by means of an EEG of 30 minutes during the evolutionResults: We have checked 10 cases diagnosed as Worster – Drought Syndrome. Of which 3/10 they expire with the diagnostic criteria. The patients in the main were presenting injuries of polimicrogiria perisilviana bilateral. To the beginning of the picture stands out the presence of a temporal bilateral irritative focality common in all the cases, with boss's later(posterior) development hipsarritmic pattern(1/3), very active irritative focality in temporo-rolándics areas in left sides (2/3). In later(posterior) controls we observe a lentification of the basal activity as common denominatorConclusions: There can not establish one EEG pattern determined in the patients with Woster Drought's Syndrome. In our sample, a case I evolve towards West's Syndrome, and other one a Benign Epilepsy of the Infancy.