Epilepsy Surgery for a Patient With Neurofibromatosis Type 1 Coexistent Moyamoya Syndrome
Abstract number :
1.442
Submission category :
18. Case Studies
Year :
2018
Submission ID :
498038
Source :
www.aesnet.org
Presentation date :
12/1/2018 6:00:00 PM
Published date :
Nov 5, 2018, 18:00 PM
Authors :
Naoto Kuroda, Seirei Hamamatsu General Hospital; Ayataka Fujimoto, Seirei Hamamatsu General Hospital; Tohru Okanishi, Seirei Hamamatsu General Hospital; Keishiro Sato, Seirei Hamamatsu General Hospital; Mitsuyo Nishimura, Seirei Hamamatsu General Hospital
Rationale: Epilepsy associated with the neurocutaneous disorders are well known and the prevalence of epilepsy in patients with neurofibromatosis Type 1 (NF1) ranges from 4 to 13%. However, epilepsy surgery for patients with NF1 is not so commonly performed. Methods: A patient was 32-year-old woman with medically intractable mesial temporal lobe epilepsy (mTLE) coexistent NF1 and moyamoya syndrome (MMS). She already had bilateral superficial temporal artery-middle cerebral artery anastomosis at the age of 17. As standard temporal approach was unavailable, we evaluated the patient to undergo the epilepsy surgery with neurologists, radiologists, neurosurgeons and neuropsychologists to find the safest trajectory to perform an epilepsy surgery. Results: The patient underwent the right selective amygdalohippocampectomy from the posterior auricle part and had obtained seizure freedom. Conclusions: This is the first surgical case report with mTLE coexistent NF1 and MMS. This type of patients should be discussed with multidisciplinary specialists such as neurologists, radiologists, neurosurgeons, neuropsychologists etc. to find the reasonable surgical approach and should not be discouraged for the epilepsy surgery. Funding: None